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Table 1 Misfolded proteins associated with neurodegenerative diseases

From: Protein misfolding in neurodegenerative diseases: implications and strategies

Proteinopathy

Aggregating protein(s)

Alzheimer’s disease

Amyloid beta (Ab) peptide; Tau

Parkinson’s disease

α-synuclein

Multiple tauopathies

Tau protein (microtubule associated)

Huntington’s disease

Huntingtin with tandem glutamine repeats

Amyotrophic lateral sclerosis

Superoxide dismutase 1

Spongiform encephalopathies

Prion proteins

Familial amyloidotic polyneuropathy

Transthyretin (mutant forms)