From: Protein misfolding in neurodegenerative diseases: implications and strategies
Proteinopathy | Aggregating protein(s) |
---|---|
Alzheimer’s disease | Amyloid beta (Ab) peptide; Tau |
Parkinson’s disease | α-synuclein |
Multiple tauopathies | Tau protein (microtubule associated) |
Huntington’s disease | Huntingtin with tandem glutamine repeats |
Amyotrophic lateral sclerosis | Superoxide dismutase 1 |
Spongiform encephalopathies | Prion proteins |
Familial amyloidotic polyneuropathy | Transthyretin (mutant forms) |